Chronic thromboembolic pulmonary hypertension is a complication of pulmonary embolism and a treatable cause of pulmonary hypertension. The pathology is a unique combination of mechanical obstruction due to failure of clot resolution, and a variable degree of microvascular disease, that both contribute to pulmonary vascular resistance. Accordingly, multiple treatments have been developed to target the disease components. However, accurate diagnosis is often delayed. Evaluation includes high-quality imaging modalities, necessary for disease confirmation and for appropriate treatment planning. All patients with chronic thromboembolic pulmonary disease, and especially those with pulmonary hypertension, should be referred to expert centres for multidisciplinary team decision on treatment. The first decision remains assessment of operability, and the best improvement in symptoms and survival is achieved by the mechanical therapies, pulmonary endarterectomy and balloon pulmonary angioplasty. With the advances in multimodal therapies, excellent outcomes can be achieved with 3-year survival of >90%.

慢性血栓栓塞性肺动脉高压是肺栓塞的一种并发症，也是肺动脉高压的一种可治疗病因。病理学是由于凝块溶解失败而导致的机械性阻塞和不同程度的微血管疾病的独特组合，这两者都会导致肺血管阻力。因此，已经开发了多种治疗方法来针对疾病成分。然而，准确的诊断往往会延迟。评估包括疾病确认和适当治疗计划所必需的高质量影像学检查。所有慢性血栓栓塞性肺疾病患者，尤其是肺动脉高压患者，都应转诊至专家中心，由多学科团队决定治疗。第一个决定仍然是手术性的评估，通过机械疗法、肺动脉内膜切除术和球囊肺血管成形术可以实现症状和生存率的最佳改善。随着多模式治疗的进步，3 年生存率为 >90%，可以取得出色的结果。