Moyamoya is characterized as a non-atherosclerotic and non-inflammatory vasculopathy that leads to progressive stenosis of the intracranial internal carotid arteries as well as the Circle of Willis. While it can be idiopathic (Moyamoya disease) or associated with another condition (Moyamoya syndrome), there is a characteristic ‘puff of smoke’ sign that can be appreciated on cerebral angiography.

中文翻译：

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在它消失在稀薄的空气中之前我看到了“一阵烟雾”的标志


烟雾病的特征是一种非动脉粥样硬化和非炎症性血管病变，导致颅内颈内动脉以及威利斯环进行性狭窄。虽然它可能是特发性的（烟雾病）或与另一种疾病（烟雾综合症）相关，但有一个特征性的“冒烟”征兆，可以在脑血管造影中识别出来。