Prader–Willi syndrome (PWS) is a complex neurodevelopmental genetic disorder characterized by hypotonia and hyperphagia. Consequently, individuals with PWS are at high risk of choking, and choking is a leading cause of morbidity and mortality. The aim of this quality improvement (QI) project is to provide choking prevention and first aid education from 0% to 80% of PWS caregivers seen in a multidisciplinary PWS clinic, and to assess the effectiveness of this education program. A QI initiative was developed to standardize and implement choking prevention and first aid education for PWS caregivers. Using a Likert scale, pre- and post-education assessments were conducted to measure caregiver (1) awareness of the PWS choking risk, (2) self-reported knowledge of choking prevention strategies, and (3) comfort in providing choking first aid. The American Heart Association Family and Friends^® CPR (Dallas, TX, USA) curriculum was utilized. Education was provided during a regularly scheduled PWS clinic appointment. At project conclusion, 45/52 (87%) of PWS caregivers received education. A post-education assessment revealed an improvement in PWS caregivers’ awareness of choking risk, self-reported knowledge of choking prevention strategies, and comfort in providing choking first aid. This QI project supports a practice change to implement choking prevention and first aid education as standard process within our PWS clinic.

中文翻译：

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在普拉德-威利综合征护理人员中实施窒息预防和急救教育的质量改进项目

Prader-Willi 综合征 (PWS) 是一种复杂的神经发育遗传性疾病，其特征是肌张力减退和食欲亢进。因此，患有 PWS 的个体处于窒息的高风险中，并且窒息是发病率和死亡率的主要原因。该质量改进 (QI) 项目的目的是为在多学科 PWS 诊所就诊的 PWS 护理人员的 0% 至 80% 提供窒息预防和急救教育，并评估该教育计划的有效性。制定了一项 QI 计划，以规范和实施针对 PWS 护理人员的窒息预防和急救教育。使用李克特量表，进行了教育前和教育后评估，以衡量护理人员 (1) 对 PWS 窒息风险的认识，(2) 自我报告的窒息预防策略知识，以及 (3) 提供窒息急救的舒适度。^® CPR（达拉斯，德克萨斯州，美国）课程被利用。在定期安排的 PWS 诊所预约期间提供教育。在项目结束时，45/52 (87%) 的 PWS 护理人员接受了教育。教育后评估显示 PWS 护理人员对窒息风险的认识、自我报告的窒息预防策略知识以及提供窒息急救的舒适度有所提高。该 QI 项目支持实践改变，以在我们的 PWS 诊所内实施窒息预防和急救教育作为标准流程。