Extract

Progressive pulmonary fibrosis (PPF), also known as progressive fibrosing interstitial lung disease (ILD), is a term used to describe progressive lung fibrosis in a patient with an ILD other than idiopathic pulmonary fibrosis (IPF) [1]. Patients with PPF often experience burdensome symptoms such as cough and dyspnoea and impairment in their quality of life [2]. Several studies have reported associations between symptoms and subsequent disease progression in patients with pulmonary fibrosis [3–5], but little is known about the relationship between changes in symptoms and outcomes including survival.

中文翻译：

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呼吸困难恶化是肺纤维化进展的预测指标

 提取

进行性肺纤维化（progressive pulmonary fibrosis， PPF），也称为进行性纤维化间质性肺疾病（ILD），是一个术语，用于描述非特发性肺纤维化（IPF）的ILD患者的进行性肺纤维化[1]。PPF 患者经常会出现咳嗽和呼吸困难等繁重的症状，以及生活质量受损 [2]。几项研究报道了肺纤维化患者的症状与随后的疾病进展之间的关联 [3-5]，但对症状变化与包括生存率在内的结局之间的关系知之甚少。